clinical features

Last reviewed 01/2018

LGMD is a clinically heterogeneous disease, from a mild late onset form to severe and even congenital forms.

LGMD is characterised by:

  • progressive symmetrical atrophy and weakness of the musccles of:
    • proximal limbs
    • shoulder and pelvic girdles
    • trunk muscles
  • the facial muscles are spared

Onset of symptoms is usually during the first two decades of life. Patients are usually confined to a wheelchair within 10-20 yr.