epidemiology

Last reviewed 01/2018

• prevalence is approximately 35 cases per 100,000;
  
  
• annual incidence of between 5 and 8 cases per 100,000 of population;
  
  
• men affected twice as often as women;
  
  
• associated with HLA-DR4 and HLA-DQw4; a hereditary form of the disease accounts for 20% of cases and is inherited as an autosomal dominant trait

Reference:

• British Heart Foundation (1999). Factfile 1/99, Dilated Cardiomyopathy.