clinical features
Last reviewed 01/2018
Presenting symptoms of the Steele Richardson Syndrome include:
- unexplained falls
- mental disturbances
- slurring of speech
On examination of the eyes:
- both eyes are affected
- pupils are often unequal but fixed
- generally there is no diplopia
- reflex eye movements e.g. on neck flexion or extension are intact
Elements of the clinical syndrome include:
- mild dementia
- mask-like facies
- pseudobulbar palsy
- mild extrapyramidal rigidity may be present in the limbs
- tendon reflexes are often increased
- there is often a positive Babinkski sign