prevalence

Last reviewed 07/2023

• usually benign tumors. 10% are malignant
• a rare tumour among children
• equally distributed between males and females and different ethnic origins
• prevalent in less than 0.2% of patients with hypertension
• predominantly sporadic in occurrence (90%)
• 10% are associated with familial disorders like
  • MEN IIa or IIb syndrome
  • Von Recklinghausen disease (neurofibromatosis)
  • Von Hippel-Lindau syndrome
  • not a feature in MEN 1 syndrome