respiratory manifestations
Last edited 08/2022
Respiratory manifestations include:
- bronchiectasis with progressive productive cough and green/brown sputum – multiple chest infections
- pneumothorax
- Aspergillus fumigatus and allergic bronchopulmonary aspergillosis (ABPA) in up to 20%
- colonisation of the lungs by Pseudomonas, which is often a difficult problem
- nasal polyposis
- pulmonary fibrosis may eventually lead to death from cor pulmonale or ventilatory failure.
Reference:
- (1) NICE (October 2017) Cystic Fibrosis. Available at https://www.nice.org.uk/guidance/ng78. (Accessed on 05 June 2022)
- (2) NHS (2021) Cystic Fibrosis. Available at https://www.nhs.uk/conditions/cystic-fibrosis/. (Accessed on 05 June 2022)
pseudomonas aeruginosa pneumonia